Melanotic neuroectodermal tumor of infancy (MNTI) of the hard palate: presentation and management

Objective: To discuss the presentation and management of melanotic neuroect odermal tumor of infancy (MNTI) of the hard palate. Method: Case presentati on and literature review. Case: A 6-month-old girl presented with a slow gr owing, non-tender anterior oral hard palate mass. Radiologic imaging reveal ed a well-circumscribed cystic lesion containing teeth. After excision, his topathologic and electron microscopic evaluation revealed MNTI. No recurren ce was seen at 12-month follow-up. Conclusions: This case and a review of t he literature reveal MNTI to be a rare, benign hard palate tumor, which may present as a smooth, firm, painless, slow-growing anterior palatal lesion. Imaging reveals a well-circumscribed cystic lesion. Complete excision shou ld be curative. Management requires attention to the potential need for pal atal reconstruction, orthodontic care and correction of secondary nasal def ormities. (C) 2000 Elsevier Science Ireland Ltd. All rights reserved.