We describe here the temporomandibular joint and masticatory muscle abnorma
lities disclosed by computed tomography and magnetic resonance imaging in a
25-year-old man with centronuclear myopathy (a congenital myopathy) who pr
esented with marked limitation of jaw movements. We found an intense and ge
neral fatty replacement of the masticatory muscles, and magnetic resonance
imaging signals indicated articular fibrosis. We conclude that in centronuc
lear myopathy, the presence of weakness and hypomotility of the masticatory
muscles can induce chronic abnormalities of the temporomandibular joint.