M. Rittmeister et al., Cementless custom-fit total hip implants on a patient with a rare form of dwarfism (Fuhrmann syndrome)., Z ORTHOP GR, 138(3), 2000, pp. 235-239
We present a single case study of a 47-year-old female patient with a rare
form of primary dysostotic dwarfism. This syndrome was first described by F
uhrmann in 1972. Seven years ago, this patient underwent bilateral cementle
ss total hip arthroplasties for severe osteoarthritis about her hips. Custo
m-made components were used. While achondroplastic patients present with wi
de femoral medullary canals, it is clinically relevant that Fuhrmann Syndro
me features narrow femoral medullary canals. This complicating anatomical f
actor in Fuhrmann syndrome as well as the increased anteversion angles were
overcome by the use of CAD stems. We conclude that the custom-made stems,
althaugh in our case measuring half the size of the smallest commercially a
vailable design, have proved to be durable and able to withstand physiologi
cal loads at follow-up period of 72 months.