An unusual concurrence of graft versus host disease caused by engraftment of maternal lymphocytes with DiGeorge anomaly

We describe a girl with DiGeorge anomaly and normal cytogenetic and molecul ar studies, whose clinical course was complicated by graft versus host dise ase caused by intrauterine materno-fetal transfusion, and several immunohae matological alterations including a monoclonal gammapathy of undetermined s ignificance (first IgG, which subsequently changed to IgM). The main clinic al features and pathological findings are discussed.