Severe thoracolumbar kyphosis in Larsen's syndrome is rare. A successful 10
-year treatment course, including T2-L4 subfascial rod placement when the p
atient was 6 years 3 months of age, nine periodic lengthenings, and definit
ive surgery at age 14 years 4 months is presented. From preoperative to 2-y
ear postoperative definitive surgery, the patient's T1 to S1 spine length i
ncreased from 19 to 36 cm, The patient's 83 degrees thoracolumbar kyphosis
was transformed to 45 degrees kyphosis and 28 degrees lumbar lordosis, and
scolioses of 95 degrees and 65 degrees were reduced to 64 degrees and 50 de
grees.