We report a case of adenomyoma of the small intestine arising in a Meckel d
iverticulum. The patient was a 22-month-old boy who presented with signs an
d symptoms of intussusception. At surgery, a Meckel diverticulum was found
and removed. On histologic examination, a tumor consisting of dilated cysti
c glands and smooth muscle bundles was identified. A diagnosis of adenomyom
a arising in a Meckel diverticulum was made. A review of the literature sho
wed that only six other pediatric cases of adenomyoma of the small intestin
e have been reported. The presence of an adenomyoma in a young patient with
in a Meckel diverticulum favors the view that adenomyomas are a variant of
pancreatic heterotopia.