Cardiac hydatosis is a rare condition, and the localization of a hydatid cy
st within the interventricular septum is exceptional. A 61-year-old man fou
nd to have a hydatid cyst of the interventricular septum is reported. Prese
nting manifestations were con gestive heart failure and signs suggestive of
an aortic valvulopathy. Diagnosis was made by Doppler echocardiography and
confirmed by magnetic resonance imaging. The cyst was approached surgicall
y try right ventriculotomy. Despite a technically successful intervention w
ithout rupture of the cyst or appearance of a conduction delay, the patient
died on the 20th postoperative day because of acute respiratory distress s
yndrome complicating infectious pneumonia.