Salivary gland choristoma of the middle ear is rare. It consists of non-mal
ignant, non-growing, normal salivary gland tissue in the middle ear. It is
a developmental abnormality that occurs around the proximal part of the sec
ond branchial arch before the fourth month of intrauterine life.
The authors found the 25th recorded case in our centre and another 24 repor
ted cases from a review of the literature between 1961 and 1999. Intratympa
nic salivary gland choristoma frequently occurs during the first and second
decades of life and with a female preponderance (56 per cent). Nearly all
the patients (96 per cent) in our review presented with a hearing loss, tha
t had begun since birth, in infancy, or during childhood. Tinnitus (28 per
cent), and serous otitis media (24 per cent) were also commonly present. On
e case complained of otorrhoea. Intratympanic and extratympanic anomalies w
ere found in 96.2 per cent and 34.6 per cent of cases respectively. Of thes
e anomalies, ossicular chain (88.5 per cent), facial nerve (65.4 per cent),
middle-ear muscles (30.8 per cent) and labyrinthine windows (23 per cent)
were the four most common sites. Therefore, salivary gland choristoma may r
epresent a manifestation of a congenital ear anomaly.
Diagnosis of salivary gland choristoma is generally not documented pre-oper
atively, but is based on surgical biopsy and histopathological investigatio
ns. Treatment of this rare lesion depends on the size, location and extent
of the mass, degree of anatomical abnormality and expertise of the surgeon.
In difficult cases where the mass is attached to the dehiscent or inferior
ly placed facial nerve, only biopsy is recommended. However, complete surgi
cal removal is advocated for a mass that is easy to remove. KTP laser use v
ia a 200 micron fibreoptic light carrier can facilitate removal especially
in cases with ossicular chain involvement.