Acral steatocystoma multiplex

Steatocystoma multiplex (SM) is characterized by multiple, widespread cutan eous cystic lesions. These lesions can appear virtually anywhere on the bod y but are more common in areas where the pilosebaceous apparatus is a-ell d eveloped, such as the trunk (especially the presternal area), neck, axilla, inguinal region, scalp, and proximal extremities. We present a case of a w oman with predominantly acrally located SM. To the best of our knowledge, a predominantly acral distribution has never been reported. We hypothesize t hat this patient's phenotype may be due to her genetic predisposition, poss ibly involving a familial defect in keratin 17, in combination with "ectopi c" acral sebaceous follicles.