CONGENITAL SKIN DEFECT AND FETUS PAPYRACE US

Background. Congenital skin defect is an uncommon condition. The term of ''congenital skin aplasia'' should be avoided since the origin may not necessarily be congenital malformation. The scalp is involved in 8 0 p. 100 of the cases. Case report. We observed a congenital skin defe ct located exclusively on the trunk. The infant lacked wide areas of s kin in symmetrical star-like configurations. Discussion. The notion of a twin expulsed after 4 months gestation suggested the diagnosis of c ongenital skin defect and fetus papyraceus or group V congenital skin aplasia in the Frieden classification as recalled. This diagnosis must not be overlooked as the prognosis is good. Closure with atrophic ski n usually occurs within a few weeks. The etiopathogenesis remains obsc ure.