A case of severe chronic hidradenitis suppurativa of the perineum complicat
ed by disfiguring fibrous, polypoid lesions is presented. The patient, a 41
-year-old woman, had a long history of axillary hidradenitis which subseque
ntly involved the perineum. Draining sinuses, scars and large pendulous mas
ses of the vulva developed over 10 years. Cutaneous scars, ridges, papules
and large fibrous polyps were present. Deep clefts, sinuses, dense fibrous
scars and foci of chronic inflammation were seen. Rarely, large fibrous pol
yps may develop in chronic hidradenitis suppurativa and may be due to chron
ic local lymphedema. Careful pathologic examination is necessary to exclude
squamous cell carcinoma.