Neonatal vascular compromise to limbs has been associated traditionally wit
h perinatal injury of the brachial plexus, fracture of the clavicle or hume
rus, or iatrogenic causes. Congenital Volkmann's ischemic contracture is an
exceptional etiology of ischemic limb in the newborn. Fewer than 10 cases
had been described in the literature. The authors report a newborn presenti
ng at birth with partial bluish discoloration of the right forearm. The cli
nical picture and laboratory studies lead to the diagnosis of congenital Vo
lkmann-Lesser ischemic contracture.