Extraabdominal desmoids represent one group of deep fibromatoses. These agg
ressive nonmetastasizing tumorlike lesions have a strong tendency to local
infiltration, with a recurrence rate of about 40%. Trauma, hormones and her
edity have been implicated as etiologic factors. Shoulder, chest wall, back
and thigh are favored sites. By combination of different diagnostic proced
ures the number of differential diagnoses can be reduced to only a few. Whi
le in former times surgery was thought to be the only kind of therapy, nowa
days adjuvant procedures like radiation, hormonal therapy and also chemothe
rapy are becoming more and more important. Amputation or other mutilating p
rocedures should be done only if the tumor recurs repeatedly.