New type of epidermal nevus syndrome

An uncommon type of epidermal nevus characterized by systematized bands of non-epidermolytic hyperkeratosis with increased hairiness and follicular hy perkeratosis was observed in a 16-year-old boy who showed, in addition, hem ihypoplasia of limbs, brachydactyly, clinodactyly and onychodystrophy. This case cannot be categorized within the group of presently established epide rmal nevus syndromes. Most likely, this combination of anomalies represents a new type of epidermal nevus syndrome. Copyright (C) 2000 S. Karger AG, B asel.