Relapsing polychondritis is an inflammatory disease that characteristi
cally involves cartilagenous tissues. Cardiovascular involvement is a
fairly common complication and the second most frequent cause of morta
lity in this disease. The case of a man with a progressive cardiac inv
olvement, aortic incompetence, mitral regurgitation, and finally compl
ete atrioventricular block offered the opportunity of reviewing the ca
rdiovascular complications in relapsing polychondritis. The most frequ
ent abnormalities are aortic regurgitation and aortic aneurysm. Furthe
rmore, several cases of atrioventricular block, mitral regurgitation,
and acute pericarditis have been reported, For early diagnosis and tre
atment of these severe complications, periodic cardiovascular examinat
ion is mandatory in these patients. Copyright (C) 1997 by W.B. Saunder
s Company.