Intramedullary ependymomas are rare tumors but comprise the majority of int
ramedullary glial neoplasms in the adult. These tumors are benign, slow-gro
wing lesions which are optimally treated with gross-total surgical resectio
n without adjuvant therapy. This objective can be attained safely in a majo
rity, of patients. Post-operative functional outcome is related to pre-oper
ative functional status. Hence, early diagnosis, prior to symptomatic progr
ession, is critical to the successful treatment of these tumors. Adjuvant t
herapy is indicated for the rare malignant or disseminated tumor or followi
ng sub-total resection.