Duodenal atresia, biliary atresia, and intestinal infarct in truncal aplasia cutis congenita

A newborn boy with aplasia cutis congenita had biliary atresia, distal duod enal atresia, and a severe infarct of the intestine resulting in complete a bsence of the entire midgut, The boy died due to biliary atresia and severe short gut syndrome approximately 3 weeks after birth. While the associatio n of duodenal atresia with aplasia cutis congenita has been described, the findings of biliary atresia and midgut atresia in association with aplasia cutis congenita have not been described previously.