MR imaging of pentalogy of Cantrell variant with an intact diaphragm and pericardium

We present a case of a neonate with the stigmata for pentalogy of Cantrell with the exception of diaphragmatic and pericardial defects. Diagnosing mos t of the anomalies in this rare syndrome can be accomplished using conventi onal modalities in radiology, but difficulties may arise determining diaphr agmatic continuity. Accurate, early diagnosis of components of this syndrom e is vital for surgical planning and assessing prognostic factors.