Leiomyosarcoma of the right ventricle

A 58-year-old women haas dyspnea and palpitations which reveal a leiomyosar coma of the right ventricle. The medical imaging shows a lobulated sessile tumor attached to the ventricular septum and the triscuspid valve extending into the pulmonary artery trunk. The resection is performed with a tricusp id valvoplasty. In spite of chemotherapy (epirubicin-cyclophosphamide), rel apse is observed with pulmonary metastases 17 months after the surgery. The death becomes on 18 months in congestive heart failure. From this case, th e authors make a review of the literature about this exceptional tumour, an d talk over the low possibilities of treatment, despite the capacities of t he new ways of diagnosis.