PRIMARY EWINGS-SARCOMA OF THE TEMPORAL BONE WITH INTRACRANIAL, EXTRACRANIAL AND INTRAORBITAL EXTENSION

Primary cranial Ewing's sarcoma is a very rare malignant tumor. Primar y temporal bone Ewing's sarcoma with intraorbital extension is also a very rare condition. In this article we describe a case of primary Ewi ng's sarcoma of the temporal bone which extended into intracranial, ex tracranial and intraorbital compartments: manifesting with a swelling in the zygomatic fossa and proptosis of the right eye. The tumor was e xcised partially, and the patient underwent radiochemotherapy. The pat ient died 6 months after the therapy, with lung metastasis. The case i s discussed with the pertinent literature.