Intra-abdominal desmoplastic small round cell tumor (IDSRT)

Intra-abdominal desmoplastic small round cell tumor (IDSRT) is a rare neopl asm that develops in the abdominal cavity in young people. We experienced a 27-year-old man who visited with ascites of unknown cause. Compression of the colon was found by barium enema examination. On colonoscopic examinatio n, diffuse white elevated lesions, about 5 mm in diameter, surrounded by ru bedo, so-called aphthoid lesions, were also observed. IDSRT was diagnosed b y biopsy at laparotomy, and chemotherapy with cyclophosphamide, etoposide, doxorubicin, and cisplatin was performed. The tumors shrank temporarily (pa rtial response), but subsequently grew in size again. The patient died; dur ing the second course of chemotherapy after relapse. We present one case re port, together with a review of the literature.