A variant of tibial hemimelia, previously undescribed in the literature and
not classifiable by either of the established classification systems, is d
escribed. The features of this condition include a short, deformed tibia; p
roximal subluxation of the fibula at the knee; a normal knee joint and an a
nkle joint that may look abnormal but falls shea of true diastasis of the j
oint. Treatment of two cases by differential lengthening of the tibia and f
ibula using the Ilizarov device is described. This form of tibial hemimelia
should be recognised as a separate variant as preservation of the foot and
ankle with expected excellent function should be possible, unlike the more
severe forms of this condition.