Renal arteriovenous malformation requiring surgery in Rendu-Osler-Weber disease (hereditary hemorrhagic telangiectasia)

Hereditary hemorrhagic telangiectasia is a rare disorder of vascular struct ure, inherited as an autosomal dominant condition. Vascular malformations m ay involve many organs but rarely the urinary tract. To our knowledge we re port the second case of an intrarenal lesion but the first to require surge ry.