Pseudomyxoma peritonei is an appendiceal tumor with distinct clinical and p
athologic features. It frequently presents a problem in diagnosis and manag
ement. We report a case or pseudomyxoma peritonei, which initially appeared
with intestinal obstruction. This is a rare initial manifestation in patie
nts who have not had multiple surgical procedures. We review the literature
and discuss the unique clinical featres and misconceptions surrounding pse
udomyxoma peritonei.