Treatment of spontaneous carotid-cavernous fistula in Ehlers-Danlos syndrome by transvenous occlusion with Guglielmi detachable coils - Case report and review of the literature

The authors report on a young woman with Ehlers-Danlos syndrome (EDS) Type TV in whom a spontaneous direct carotid-cavernous fistula (CCF) was treated by transvenous occlusion with regular and fiber-coated Guglielmi detachabl e coils. To the authors' knowledge, this is the first time this approach ha s been used in a patient with EDS. The different treatment options are disc ussed, and the literature on endovascular treatment of direct CCFs in EDS i s reviewed.