Primary rhabdomyosarcoma of the leptomeningis. Histological, immunohistochemical and ultrastructural study of one case

A 64 year-old patient, complained of headache and neurological disorders. C T scan found a voluminous solitary tumor of the posterior part of the left cavernous sinus. Removal of tumor was followed by a rapid recurrence and by the patient's death. Histologic study found a malignant undifferentiated t umoral proliferation, with straplike cells. Immunohistochemical stains were positive for conjonctival and muscular differenciation Ultrastructural stu dy revealed intracytoplasmic filamentous striated structure. The primary me ningeal rhabdomyosarcoma is art exceptional tumor, generally affecting youn g patients. Its prognosis is poor and its histogenesis remains unclear.