Churg-Strauss syndrome is a systemic vasculitis characterized by asthma, ti
ssue and blood eosinophilia, and granulomatous vasculitis. Lymph node invol
vement as part of systemic disease or as the primary site of involvement is
rare. We report a single case of primary (isolated) nodal Churg-Strauss sy
ndrome occurring in an 11-year-old boy with asthma, fever, night sweats, an
d cervical adenopathy. The clinical diagnosis was lymphoma. The unusual pre
sentation of Churg-Strauss syndrome limited to lymph nodes is important to
recognize and diagnose correctly because the administration of steroid ther
apy is associated with a favorable outcome.