Interhemispheric neuroepithelial cyst associated with agenesis of the corpus callosum - A case report and review of the literature

This report describes a neonatal case in whom a large interhemispheric cyst associated with agenesis of the corpus callosum was revealed by fetal ultr asonography and demonstrated by MRI to be multilobulated, Endoscopic fenest ration of cysts was initially designed in view of the development of the pa tient's brain and surgical invasiveness, One year later, when motor paresis of the left arm and progressive enlargement of the cyst on MRI were reveal ed, open surgery was performed, The histological diagnosis was a neuroepith elial cyst with the feature of choroid plexus epithelia, The clinicopatholo gical features of interhemispheric epithelial cysts associated with agenesi s of the corpus callosum are reviewed in the light of differential diagnosi s and therapeutic considerations, Copyright (C) 2000 S.Karger AG,Basel.