Relapsing polychondritis (RP) is a disease of unknown etiology and it is ch
aracterized by inflammation of the cartilage. While the clinical picture of
RP in adults is well described, RP in childhood is poorly documented. We d
escribe a young girl presenting with acute dyspnea, strider and polyarthrit
is. The diagnosis of RP was made 2 years after first presentation, when aur
icular chondritis occurred. Based on a MEDLINE search, reports on RP in chi
ldhood were reviewed. The frequency of chondritis and systemic manifestatio
ns of RP in children was compared to data in adults and found to be very si
milar. RP in childhood carl be a life-threatening and debilitating disease.