Yellow nail syndrome and intestinal lymphangiectasia

The yellow nail syndrome, a combination of yellow discoloured nails, lymphe dema and pleural effusions, is a rare clinical condition. We report a case of the yellow nail syndrome associated with intestinal lymphangiectasia rev ealed by chylous ascites and protein-losing gastroenteropathy. This associa tion reported in only three cases in the literature leads us to discuss the relations between yellow nail syndrome, primitive intestinal lymphangiecta sia and primary lymphatic disorders.