Multiple eccrime hidrocystomas in Schopf-Schultz-Passatge: a case report

Schopf-Schultz-Passarge syndrome is a rare ectodermal dysplasia described b y Schopf in 1971. The disease is characterized by hypodontia, hypotrichosis , palmoplantar keratoderma, hypoplastic nails and eyelid hydrocystomas. We report the case of a 71-year-old man, the first French description of th is syndrome, who remarkably presented all the signs. The patient also had s kin tumors, multiple eccrime hidrocystomas and aspectific macular degenerat ion. A review of the literature is discussed.