Ipsilateral renal dysplasia with hypertensive heart disease in an infant with cutaneous varicella lesions: An unusual presentation of congenital varicella syndrome

A child with congenital varicella syndrome including cutaneous lesions and ipsilateral renal dysplasia with hypertensive heart disease is described. V aricella was contracted during the tenth week of gestation. Typical congeni tal varicella bullae, high titer of anti-varicella-zoster virus IgM, and a small right kidney were noted after birth. Hypertensive heart disease resul ting from renal dysplasia occurred at 1 year of age. The cutaneous lesions and the dysplastic kidney involved the same dermatomes. Nephrectomy proved to be the treatment of choice for hypertension and congestive heart failure .