Cystic renal lymphangiectasia presenting as renal insufficiency in childhood

Cystic renal lymphangiectasia is an unusual cause of cystic renal disease i n childhood. We present a case of bilateral cystic renal lymphangiectasia i n a 7-year-old boy who presented with asymptomatic renal insufficiency and anemia with decreased erythropoietin production. The clinical features of t his condition and the diagnostic approach are reviewed. Although rare, this disorder should be considered in the differential diagnosis of cystic rena l disease.