We report an extremely rare case of a splenic epidermoid cyst of the pancre
as in a 51-year-old Japanese male with no clinical symptoms. A cystic tumor
of the pancreatic tail was detected incidentally by abdominal ultrasonogra
phy. The patient was referred to the Gunma University Hospital for further
examination of the pancreatic tumor. Upon diagnosis of a benign cystic tumo
r, a distal pancreatectomy with splenectomy was performed. Microscopically,
the multicystic tumor, which was surrounded by the splenic tissue, was loc
ated within the pancreatic tissue. The cysts were lined by non-keratinizing
squamous epithelium. The diagnosis of an epidermoid cyst occurring in an i
ntrapancreatic accessory spleen was confirmed. To our knowledge, this is th
e 4th case ever reported in the English literature.