The presence pf accessory mitral valve tissue in the left ventricular outfl
ow tract (LVOT) is a rare cause of obstruction. Previous cases reported in
the literature are associated either with other complex congenital abnormal
ities, or with other forms of LVOT obstruction. This report presents the fi
rst case of a duplication of the anterior leaflet of the mitral valve occur
ring as an isolated congenital anomaly. It produced mild subaortic obstruct
ion. The report emphasizes the importance of transthoracic two-dimensional
echocardiography and Doppler assessment in the recognition of congenital ab
normalities of the mitral valve and subvalvular apparatus as a differential
diagnosis of subaortic stenosis.