We report the case of a patient with oral ulcerations that were likely trau
matic in origin caused by biting of the tongue. Physical examination showed
only deviation, fasciculations, and hemiatrophy of the right side of the t
ongue. Neurologic examination disclosed an isolated XII nerve palsy. A magn
etic resonance image showed a lesion in the posterior fossa displacing the
brain stem at a bulbar level. This was consistent with the diagnosis of a m
eningioma, later confirmed by the histopathologic study. It is very unusual
that a meningioma produces a selective involvement of the XII nerve. Early
diagnosis of a foramen magnum meningioma is important, both to improve pro
gnosis and to avoid neurologic sequelae.