Massive pelvic hemangioma in a patient with blue rubber bleb nevus syndrome

Blue rubber bleb nevus syndrome (BRBNS) is a rare disorder characterized by gastrointestinal and cutaneous hemangiomas, Patients typically present wit h gastrointestinal bleeding and anemia. Management of gastrointestinal blee ding may be challenging, since these lesions may be diffusely distributed t hroughout the gastrointestinal tract. The most common location is the small bowel, and recurrence is common. We describe a patient with BRBNS and lowe r gastrointestinal bleeding resulting from a large pelvic hemangioma erodin g into the rectal wall.