Keratosis lichenoides chronica - Report of a case associated with B-cell lymphoma and leg panniculitis

Keratosis lichenoides chronica (KLC) is a rare chronic dermatosis character ized by lichenoid hyperkeratotic papules arranged in a linear and reticular pattern, and seborrheic-dermatitis-like lesions on the face. Less frequent ly, palmoplantar keratoderma, nail dystrophies, mucosal as well as eye lesi ons are present. KLC affects adults and very few cases have been reported i n childhood. Although infrequently, KLC has been associated with systemic d iseases, including chronic infectious diseases, kidney disorders and lympho ma. Here we report the case of an adult KLC patient with skin, nail and muc osal involvement, and onset in the first year of life who developed a leg p anniculitis and a mantle cell lymphoma. Following chemotherapy for the lymp homa, panniculitis resolved completely, and skin and mucosal KLC lesions am eliorated. Copyright (C) 2000 S. Karger AG, Basel.