We report a case of middle ear adenoma, a rare epithelial tumour composed o
f adenomatous and neuroendocrine cells. These tumours have been designated
by many different names, leading to controversy regarding their histogenesi
s and classification. The diagnosis was based on light microscopy and immun
ohistochemistry. A positive immunoreaction was evidenced for antibodies to
keratin and chromogranin. The tumour was removed surgically. No additional
therapy is recommended in the literature.