Pancreatic metastasis of a pleuropulmonary blastoma in an adult

Pleuropulmonary blastoma (PPB) is a rare dysontogenetic tumor that usually develops in the first decade of life and has been recognized as a distinct clinico-pathological entity different from the ordinary pulmonary blastoma of adulthood. Since the tumor grows aggressively and tends to metastasize e arly, physicians have to be aware of late onset of symptoms and uncommon ma nifestations. We report a case of PPB in a young adult and its recurrence i n the pancreas after primary surgical treatment and adjuvant chemotherapy. Keeping in mind the moderate prognosis of PPB in children, accurate assessm ent and treatment of PPB require a team approach of oncology, radiology and surgery to establish new therapeutic guidelines in the future.