Klippel-Feil syndrome in association with posterior fossa suboccipital dermoid cyst

We present the second case of Klippel-Feil syndrome in association with a p osterior fossa dermoid cyst extending through the occipital bone and presen ting as a suboccipital subcutaneous mass. We describe its radiographic, CT, and MRI appearances as well as on MRI diffusion-weighted images. Posterior cranial fossa dermoid cysts and sinuses should be added to the list of con genital abnormalities which must be sought in patients with Klippel-Feil sy ndrome. Diffusion-weighted images of brain may differentiate these masses f rom cerebral spinal fluid collections.