An unusual association of intracranial aneurysms and oesophageal duplication in a case of Klippel-Trenaunay syndrome

The Klippel-Trenaunay syndrome (KTS) is a congenital disorder resulting fro m a mesodermal abnormality, characterised by cutaneous capillary haemangiom as, hypertrophy of bone and soft tissues and varicose veins. The presence o f intracranial aneurysms has rarely been described, while oesophageal dupli cation has not been reported previously. We describe a patient with the KTS with both there additional abnormalities, which could be explained by a po stulated mosaic gene abnormality.