A 19-year-old woman presented with a 3-week history of abdominal distension
. Clinical examination and computed tomography showed a right adnexal mass
occupying most of the pelvis and lower abdomen. The serum CA 125 level was
236 U/mL. A 36 x 27 x 9 cm, 3160-g tumor was removed at laparotomy. Histolo
gy showed an extrauterine mixed epithelial-mesenchymal tumor with adenosarc
omatous components. Extrauterine mixed epithelial-mesenchymal tumors in you
ng women are rare but considered to be of low malignant potential with a lo
w risk of recurrence.