SURGICAL-CORRECTION OF INCOMPLETE CRYPTOPHTHALMOS IN FRASER-SYNDROME

PURPOSE: To demonstrate favorable long-term visual outcome after ocula r reconstruction in an infant with Fraser syndrome and with complete l eft cryptophthalmos. METHODS: Reconstruction of incomplete right crypt ophthalmos in our patient was accomplished in a stepwise manner, begin ning in the third week of life, by dissecting the eyelids from the cor nea, reconstructing the conjunctival fornices with buccal mucosa, and repairing the upper lid coloboma in a flap reconstruction using the in ferior eyelid margin. RESULTS: At age 3 years, the patient currently h as good movement of the right eyelids when blinking, reasonable right tear function, and a visual acuity in the right eye between 20/200 and 20/360 on forced preferential looking. CONCLUSION: In selected cases of incomplete cryptophthalmos, oculoplastic and corneal surgery may re sult in useful vision and in good eyelid movement when blinking.