Mitral valve repair may be performed without ring support with advantages r
elated to results and complications. The objective of this study was to ana
lyze the long-term clinical results following surgical repair and reconstru
ction without the use of rings in cases of congenital mitral lesions in chi
ldren less than 12 years of age. Twenty-one patients who had undergone surg
ery during the period from 1975 to 1998 were evaluated. The mean age was 4.
6 +/- 3.4 years. Females represented 47.6% of the total. Mitral regurgitati
on was present in 57.1% (12 patients), stenosis in 28.6% (6 patients), and
the mixed lesion group represented 14.3% (3 patients). Perfusion time was 4
3.1 +/- 9.5 minutes and ischemic time 29.4 +/- 10.5 minutes. Follow-up time
was 41.5 +/- 53.6 months for the regurgitation group, 46.3 +/- 32.0 months
for the stenosis group, and 39.41 +/- 37.51 months for the mixed lesion gr
oup. Echocardiographical follow-up time was 37.17 +/- 39.51 months for the
regurgitation group, 42.61 +/- 30.59 months for the stenosis group, and 39.
41 +/- 37.51 months for the mixed lesion group. Operative mortality was 9.5
% (two cases). There were no late deaths. In the regurgitation group, 10 pa
tients (83.3%) were asymptomatic (p = 0.004). In the echocardiographical fo
llow-up, most of the patients had minimal regurgitation. In the clinical fo
llow-up of the stenosis group all patients were in functional class I (NYHA
). The mean transvalvular gradient measured by echocardiography was from 8
to 12 mmHg with a mean gradient of 10.7 mmHg. In the mixed lesion group the
re was one reoperation at postoperative month 43. There were no cases of en
docarditis or thromboembolism. Mitral valve repair in congenital lesions is
associated with good late results. The majority of cases in the regurgitat
ion group remain asymptomatic and do not require reoperation. Rings or annu
lar support are not necessary in such cases. Satisfactory repair is more di
fficult to achieve in cases of mitral stenosis due to valvular abnormalitie
s and the seriousness of the associated lesions.