Extracutaneous Sweet syndrome involving the gastrointestinal tract in a patient with Fanconi anemia

Acute febrile neutrophilic dermatosis, or Sweet syndrome, is a cutaneous er uption characterized clinically by the appearance of painful red plaques an d nodules and histologically by an intense dermal neutrophilic infiltrate. Extracutaneous manifestations are rare. We report a patient in whom otherwi se typical cutaneous Sweet syndrome was accompanied by an extracutaneous ma nifestation in the ileum.