NEURONAL INTESTINAL DYSPLASIA PRESENTING AS AN ABDOMINAL-MASS - REPORT OF A CASE

An unusual clinical presentation of a patient with neuronal intestinal dysplasia is presented. A 4G year-old male noted a palpable mass in t he right lower quadrant of his abdomen for two months, A computed axia l tomographic scan showed a thickened wall of the cecum with a tumor-l ike appearance. The excised specimen consisted of a mass caused by the thickened, edematous wall of the dilated cecum and appendix. The wall of the cecum and appendix measured up to 2.5 and 0.8 cm, respectively , in thickness. Microscopic studies showed extensive hyperplasia and h ypertrophy of the ganglia and nerve plexuses and hypertrophy of the mu scularis propria, consistent with neuronal intestinal dysplasia.