Chordoma periphericum - A case report

The authors describe a tumor that had the histologic and ultrastructural fe atures and immunohistochemical profile of on axial chordoma, but arose in t he distal ulna. A skeletal survey failed to show any other site of involvem ent. The turner was resected. and the patient remains free of disease 2 1/2 years later. Rare tumors with the histologic features of chordoma have bee n reported in appendicular locations. Chordoma periphericum. a tumor that h as the potential to metastasize. needs to be distinguished from parachordom a because no classic parachordoma has been reported to disseminate.