Aglomerular segmental hypoplasia of the kidney: report of a clinical case.

Aglomerular segmental hypoplasia of the kidney is a disease that is uncommo n in the adult; the average age at appearance of symptoms is between ten an d 15 years. A clear female predominance has been noted, and this disease is often misdiagnosed as chronic pyelonephritis. However, the radiological an d pathological characteristics are different to the latter. The etiology of aglomerular segmental hypoplasia has not yet been determined. It is import ant to acquire further knowledge regarding this disease, as in certain case s this information could help to avoid unecessary nephrectomy. (C) 2001 Edi tions scientifiques et medicales Elsevier SAS.