Type 1-primary cutaneous meningioma of the scalp

Type 1-primary cutaneous meningioma is a rare and often clinically unsuspec ted lesion of the scalp, forehead or paravertebral region which occurs at b irth or during childhood. The pathogenesis of these lesions still remains u ncertain. Several authors have emphasized that type l-cutaneous meningiomas are not real tumors but sequestrated meningoceles or heterotopic meningeal nodules of the skin. Nevertheless, the search for an intracranial or intra vertebral connection should be carried out. We describe the clinical and pa thological features of a congenital type l-meningioma of the vertex. No cra nial defect or intracranial tumor was found. However, the cutaneous lesion was directly linked to a large cranial vein. The purpose of this study was to illustrate this rare lesion and to indicat e the possible surgical risks and the pathological characteristics.